Background information:

- Autoinflammatory vs. Autoimmune (AID vs. AI)

- Periodic Fever Syndromes (PFS)

- Undifferentiated autoinflammatory diseases (uSAID)

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Monogenic Autoinflammatory Diseases:

 

FMF

TRAPS 

HIDS/MKD

CAPS: FCAS, MWS, NOMID/CINCA

HA20

NLRP12- associated autoinflammatory disorder 

DIRA

DITRA

DADA2

Majeed’s Syndrome

PAPA

Blau Syndrome

Yao Syndrome

PLAID

SAVI

PAAND

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Multifactorial Autoinflammatory Diseases:

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PFAPA 

Behçet’s Disease 

Crohn’s Disease

Systemic juvenile idiopathic arthritis (sJIA) or Still's disease

Adult-onset Still's disease (AOSD)

Schnitzler‘s Syndrome

Sweet’s Syndrome

CRIA Syndrome

CRMO Syndrome

SAPHO Syndrome

Sarcoidosis